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Proteintech
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Immunogen sequence: MLWSGCRRF GARLGCLPGG LRVLVQTGHR SLTSCIDPSM GLNEEQKEFQ KVAFDFAARE MAPNMAEWDQ KELFPVDVMR KAAQLGFGGV YIQTDVGGSG LSRLDTSVIF EALATGCTST TAYISIHNMC AWMIDSFGNE EQRHKFCPPL CTMEKFASYC LTEPGSGSDA ASLLTSAKKQ GDHYILNGSK AFISGAGESD IYVVMCRTGG LGPKGISCIV VEKGTPGLSF GKKEKKVGWN SQPTRAVIFE DCAVPVANRI GSEGQGFLIA VRGLNGGRIN IASCSLGAAH ASVILTRDHL NVRKQFGEPL ASNQYLQFTL ADMATRLVAA RLMVRNAAVA LQEERKDAVA LCSMAKLFAT DECFAICNQA LQMHGGYGYL KDYAVQQYVR DSRVHQILEG SNEVMRILIS RSLLQE (1-415 aa encoded by B C001964)
This gene encodes a member of the acyl-CoA dehydrogenase family of enzymes that catalyze the dehydrogenation of acyl-CoA derivatives in the metabolism of fatty acids or branch chained amino acids. The encoded protein is a mitochondrial enzyme that functions in catabolism of the branched-chain amino acid valine. Defects in this gene are the cause of isobutyryl-CoA dehydrogenase deficiency.
仅用于科研。不用于诊断过程。未经明确授权不得转售。
蛋白别名: ACAD-8; Activator-recruited cofactor 42 kDa component; Acyl-CoA dehydrogenase family member 8; acyl-CoA dehydrogenase family, member 8; acyl-Coenzyme A dehydrogenase family, member 8; ARC42; IBDH; Isobutyryl-CoA dehydrogenase, mitochondrial
基因别名: 2310016C19Rik; ACAD-8; ACAD8; AI786953; ARC42; IBD; RGD1564209
UniProt ID: (Human) Q9UKU7, (Mouse) Q9D7B6
Entrez Gene ID: (Human) 27034, (Rat) 367196, (Mouse) 66948