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Proteintech
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Immunogen sequence: MATATRLLG CRVASWRLRP PLAGFVSQRA HSLLPVDDAI NGLSEEQRQL RQTMAKFLQE HLAPKAQEID RSNEFKNLRE FWKQLGNLGV LGITAPVQYG GSGLGYLEHV LVMEEISRAS GAVGLSYGAH SNLCINQLVR NGNEAQKEKY LPKLISGEYI GALAMSEPNA GSDVVSMKLK AEKKGNHYIL NGNKFWITNG PDADVLIVYA KTDLAAVPAS RGITAFIVEK GMPGFSTSKK LDKLGMRGSN TCELIFEDCK IPAANILGHE NKGVYVLMSG LDLERLVLAG GPLGLMQAVL DHTIPYLHVR EAFGQKIGHF QLMQGKMADM YTRLMACRQY VYNVAKACDE GHCTAKDCAG VILYSAECAT QVALDGIQCF GGNGYINDFP MGRFLRDAKL YEIGAGTSEV RRLVIGRAFN ADFH (1-423 aa encoded by BC017202)
Isovaleryl-CoA dehydrogenase (IVD) is a mitochondrial matrix enzyme that catalyzes the third step in leucine catabolism. The genetic deficiency of IVD results in an accumulation of isovaleric acid, which is toxic to the central nervous system and leads to isovaleric acidemia.
仅用于科研。不用于诊断过程。未经明确授权不得转售。
蛋白别名: Butyryl-CoA dehydrogenase; isovaleryl CoA dehydrogenase; isovaleryl Coenzyme A dehydrogenase; isovaleryl dehydrogenase; Isovaleryl-CoA dehydrogenase, mitochondrial; IVD
基因别名: 1300016K07Rik; 6720455E18Rik; ACAD2; AI463340; IVD
UniProt ID: (Human) P26440, (Rat) P12007, (Mouse) Q9JHI5
Entrez Gene ID: (Human) 3712, (Rat) 24513, (Mouse) 56357