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Proteintech
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Immunogen sequence: EEWADLFQA AGAKYVVLTT KHHEGFTNWP SPVSWNWNSK DVGPHRDLVG ELGTALRKRN IRYGLYHSLL EWFHPLYLLD KKNGFKTQHF VSAKTMPELY DLVNSYKPDL IWSDGEWECP DTYWNSTNFL SWLYNDSPVK DEVVVNDRWG QNCSCHHGGY YNCEDKFKPQ SLPDHKWEMC TSIDKFSWGY RRDMALSDVT EESEIISELV QTVSLGGNYL LNIGPTKDGL IVPIFQERLL AVGKWLSING EAIYASKPWR VQWEKNTTSV WYTSKGSAVY AIFLHWPENG VLNLESPITT STTKITMLGI QGDLKWSTDP DKGLFISLPQ LPPSAVPAEF AWTIKLTGVK (113-461 aa encoded by BC017338)
Alpha-L-fucosidase (EC 3.2.1.51) is a lysosomal enzyme involved in the degradation of fucose-containing glycoproteins and glycolipids (Occhiodoro et al., 1989 [PubMed 2803312]). At least 2 separate polymorphic alpha-L-fucosidases are recognized in man: that in tissues, FUCA1, which is deficient in fucosidosis (MIM 230000), and that in plasma, FUCA2 (MIM 136820).[supplied by OMIM].
仅用于科研。不用于诊断过程。未经明确授权不得转售。
蛋白别名: A L fucosidase I; A L fucoside fucohydrolase 1; Alpha-L-fucosidase 1; Alpha-L-fucosidase I; Alpha-L-fucoside fucohydrolase 1; EC 3.2.1; EC 3.2.1.51; Fucosidase alpha-L-1 tissue; Fucosidase, alpha-L-1, tissue; Tissue alpha-L-fucosidase; Tissue α L fucosidase; α L fucosidase 1; α L fucosidase I; α L fucoside fucohydrolase 1
基因别名: 0610006A03Rik; 9530055J05Rik; Afuc; FUCA; FUCA1; Nbla10230
UniProt ID: (Human) P04066, (Rat) P17164, (Mouse) Q99LJ1
Entrez Gene ID: (Human) 2517, (Rat) 24375, (Mouse) 71665