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Proteintech
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Immunogen sequence: SLEVQLTAQ TSLGPVSDFY TLPVGIRTVA VTKSQFLING KPFYFHGVNK HEDADIRGKG FDWPLLVKDF NLLRWLGANA FRTSHYPYAE EVMQMCDRYG IVVIDECPGV GLALPQFFNN VSLHHHMQVM EEVVRRDKNH PAVVMWSVAN EPASHLESAG YYLKMVIAHT KSLDPSRPVT FVSNSNYAAD KGAPYVDVIC LNSYYSWYHD YGHLELIQLQ LATQFENWYK KYQKPIIQSE YGAETIAGFH QDPPLMFTEE YQKSLLEQYH LGLDQKRRKY VVGELIWNFA DFMTEQSPTR VLGNKKGIFT RQRQPKSAAF LLRERYWKIA NETRYPHSVA KSQCLENSLF T (302-651 aa encoded by BC014142)
The GUSB gene encodes beta-glucuronidase (EC 3.2.1.31), a lysosomal hydrolase involved in the stepwise degradation of glucuronic acid-containing glycosaminoglycans. It is a tetrameric glycoprotein composed of identical subunits. The GUSB gene is mutated in mucopolysaccharidosis type VII (MPS7; MIM 253220).
仅用于科研。不用于诊断过程。未经明确授权不得转售。
蛋白别名: adipose storage deficiency; beta glucuronidase; beta-D-glucuronidase; Beta-G1; Beta-glucuronidase; glucuronidase, beta
基因别名: Ac2-223; AI747421; asd; BG; g; Gur; Gus; Gus-r; Gus-s; Gus-t; Gus-u; GUSB; Gut; MPS7
UniProt ID: (Human) P08236, (Rat) P06760, (Mouse) P12265
Entrez Gene ID: (Human) 2990, (Rat) 24434, (Mouse) 110006